How long can you live with retroperitoneal fibrosis?

Malignant retroperitoneal fibrosis is associated with poor prognosis, and most patients have an average survival of approximately 3-6 months. Idiopathic retroperitoneal fibrosis carries a good prognosis, with little effect on long-term morbidity or mortality.

Can retroperitoneal fibrosis be cured?

While surgery has traditionally been the only option for patients suffering from a rare condition known as retroperitoneal fibrosis (RPF), Johns Hopkins researchers have now developed a medical therapy to treat and cure this progressive disorder.

Is retroperitoneal fibrosis serious?

Potential complications This may result in chronic kidney failure and long-term blockage of the ureters, which can cause urine backup and kidney swelling. Untreated retroperitoneal fibrosis can also lead to the cutting off of the blood supply to the legs, which in turn can lead to further dangerous complications.

Is retroperitoneal fibrosis a disability?

If you or your dependent(s) are diagnosed with Retroperitoneal Fibrosis and experience any of these symptoms, you may be eligible for disability benefits from the U.S. Social Security Administration.

How common is retroperitoneal fibrosis?

Retroperitoneal fibrosis is a rare condition that develops in about one in 200,000 people. While it can affect anyone at any age, those at highest risk (for reasons that are not clear) are men aged between 40 and 60 years.

Is retroperitoneal fibrosis genetic?

Inheritance. Most cases of retroperitoneal fibrosis are sporadic, which means that they occur in people with no apparent history of the disorder in their family. In rare cases, the condition has been reported to occur in a few members of the same family, but the inheritance pattern is unknown.

Is retroperitoneal fibrosis hereditary?

What is survival rate of retroperitoneal sarcoma?

In our experience, the overall resectability rate for primary and locally recurrent retroperitoneal sarcomas has been 95%. Overall, the 5-year survival (10-year in parentheses) in our series was 65% (56%) for primary retroperitoneal sarcomas and 53% (34%) for those referred with local recurrence.